Foreword to the First Edition |
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xv | |
Preface |
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xvii | |
Acknowledgments |
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xix | |
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Embryology and Development |
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1 | (8) |
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Caudal Neural Tube Formation (Secondary Neurulation) |
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Disorders of Primary Neurulation |
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Disorders of Secondary Neurulation---Occult Dysraphic States |
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Disorders of Prosencephalic Development |
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Dandy-Walker Malformation |
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Neuronal Proliferation and Migration Disorders |
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Organizational Disorders of the Cortex |
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Normal Developmental Milestones |
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9 | (54) |
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The Cerebellum and Connections |
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Functional Considerations and Tracts |
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Summary Table---Cerebellum and Connections |
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Functional Subdivisions Specific Relay Nuclei |
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Anterior Thalamic Nucleus |
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Thalamic Reticular Nucleus |
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Posteromedial Arteries (Thalamoperforating) |
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Posterolateral Arteries (Thalamogeniculate) |
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Posterior Choroidal Artery |
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Anterior Choroidal Artery |
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Ventral Posterior Lesions |
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Lateral Geniculate Lesion |
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Bilateral Thalamic Lesions |
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Components of the Limbic System |
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Connections of the Limbic System |
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Basal Ganglia Connections |
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The Pallidothalamic Connections |
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Clinical Application---Diseases of the Basal Ganglia |
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Introduction---Definition of Functional Components |
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Cranial Nerve I---Olfactory Nerve |
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Cranial Nerve II---Optic Nerve |
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Cranial Nerve III---Oculomotor Nerve |
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Cranial Nerve IV---Trochlear Nerve |
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Cranial Nerve V---Trigeminal Nerve |
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Cranial Nerve VI---Abducens Nerve |
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Cranial Nerve VII---Facial Nerve |
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Cranial Nerve VIII---Vestibulocochlear Nerve |
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Cranial Nerve IX---Glossopharyngeal |
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Cranial Nerve X---Vagus Nerve |
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Cranial Nerve XI---Accessory |
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Cranial Nerve XII---Hypoglossal |
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Cranial Nerves and Associated Foramina |
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Spinal Cord Anatomy and Diseases |
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Pathologic Considerations |
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The Plexi and Extremities |
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Peripheral Nerves of the Upper Extremity |
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Peripheral Nerves of the Lower Extremity |
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Energy Sources for Muscle Contraction |
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Motor Units and Control of Muscle Contraction |
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63 | (16) |
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Neurotransmitters and Receptors |
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Depression-General Information |
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Classification of Antidepressants |
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Drug-Specific Side Effects |
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Negative Theory of Schizophrenia |
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Drugs Associated with Nervous System Disorders |
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Neuroleptic Malignant Syndrome |
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Benign Intracranial Hypertension |
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Neuromuscular Transmission Abnormalities |
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Central Nervous System Infections |
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79 | (18) |
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Atypical Bacterial Infections |
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Herpes Zoster (Varicella Zoster, Shingles) |
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Human Immunodeficiency Virus |
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Tropical Spastic Paraparesis |
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St. Louis Encephalitis, Eastern Equine Encephalitis |
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Subacute Sclerosing Panencephalitis |
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Progressive Multifocal Leukoencephalopathy |
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Creutzfeldt-Jakob Disease |
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Gerstmann-Straussler Disease |
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Naegleria Fowleri Meningoencephalitis (PAM) |
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Rocky Mountain Spotted Fever |
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97 | (22) |
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Glycogen Storage Diseases |
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Acid Maltase Deficiency (also known as Pompe Disease) |
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Muscle Phosphorylase Deficiency (McArdle Disease) Glycogen Storage Disease Type V |
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Muscle Phosphofructokinase Deficiency (Tauri Disease) Glycogen Storage Disease Type VII |
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Glycogen Storage Disease Quick Reference Table |
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γ-Hydroxybutyric Aciduria |
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Nonketotic Hyperglycinemia |
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Hartnup Disease---Amino Acid Transport Defect |
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Lowe Syndrome (Oculocerebrorenal Syndrome) |
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Maple Syrup Urine Disease |
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Abetalipoproteinemia (Bassen-Kornzweig Disease) |
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Cerebrotendinous Xanthomatosis |
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Subtypes Include Acute Intermittent Porphyria, Hereditary Coproporphyria, Variegate Porphyria |
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Wilson Disease (Hepatolenticular Degeneration) |
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Kinky Hair Disease (Menkes Disease) |
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Metachromatic Leukodystrophy |
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Krabbe's Disease (Globoid Cell Leukodystrophy) |
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Adrenoleukodystrophy (Sudanophilic Cerebral Sclerosis) |
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Pelizaeus-Merzbacher Disease (Tigroid Leukodystrophy) |
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Peripheral nerve involvement is found in the following diseases |
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White Matter Disease Summary Table |
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Wernicke-Korsakoff Syndrome |
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Alcoholic Cerebellar Degeneration |
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Marchiafava-Bignami Disease |
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Central Pontine Myelinolysis |
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119 | (10) |
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Cerebrospinal Fluid (CSF) |
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129 | (16) |
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Transient Ischemic Attack |
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Cerebral Blood Flow (CBF) |
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Stroke in the Young Adult |
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Location of Hypertensive Hemorrhages |
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Unruptured intracranial aneurysms (UIA) |
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145 | (18) |
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Central Nervous System Tumors and Neuropathology |
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Grading Systems for Astrocytic Tumors |
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Primitive Neuroectodermal Tumors (PNET) |
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Tumors of the Nerve Sheath and Meninges |
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CNS Tumors---Quick Reference Tables and Lists |
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Most Common Tumors by Location |
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Tumors that commonly present radiographically |
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grossly as a cyst containing a mural nodule |
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When You Hear . . . Think of . . . (most commonly associated with) |
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Miscellaneous Cellular Alterations of Note (not neoplastic) |
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Nervous System Complications of Chemotherapy |
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Brain Edema and Herniation Syndromes |
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Three Types of Brain Edema |
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163 | (48) |
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General Approach to Peripheral Neuropathies |
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Evaluation and Classification |
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Peripheral Neuropathy Syndromes |
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Acute Ascending Motor Neuropathy with Variable Sensory Disturbance |
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Subacute Sensorimotor Paralysis |
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Syndrome of Chronic Sensorimotor Polyneuropathy (less chronic acquired forms) |
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Syndrome of Hereditary Chronic Polyneuropathy (tends to be more chronic than acquired, progressive, symmetrical, and degenerative neuropathies) |
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Acute and Chronic Inflammatory Demyelinating Polyneuropathies |
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Acute Inflammatory Demyelinating Polyneuropathy (Guillain-Barre Syndrome) |
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Chronic Inflammatory Demyelinating Polyneuropathy (CIDP) |
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Brachial Plexopathy Syndromes |
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Lumbosacral Plexopathy Syndromes |
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Special Forms of Myasthenia |
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Lambert-Eaton Myasthenic Syndrome |
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Myasthenic Syndromes in Childhood |
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Duchenne Muscular Dystrophy |
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Becker Muscular Dystrophy |
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Facio-scapulohumeral Muscular Dystrophy |
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Emery-Dreifuss Muscular Dystrophy (Humeroperoneal) |
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Oculopharyngeal Dystrophy |
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Congenital Myotonic Dystrophy |
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Myotonia Congenita (Thomsen Disease) |
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Centronuclear (Myotubular) Myopathy |
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Neuromyotonia (Isaac Disease) |
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Stiff-Person Syndrome (Moersch-Woltman Syndrome) |
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Laboratory Evaluation for Muscle Diseases |
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Periodic Paralysis Quick Reference Table |
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Other Periodic Paralysis Subtypes |
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211 | (16) |
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Prognostic Factors for Stopping Antiepiletic Drugs |
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Nonepileptic Events (nonepileptic seizures, pseudoseizures) |
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227 | (16) |
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Origin of the Electroencephalogram (EEG) |
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Electrocerebral Silence---EEG Settings and Results |
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Miniature End Plate Potential (MEPP) |
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End-Plate Potential (EPP) |
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Motor Unit Potential (MUP) |
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Compound Motor Action Potential (CMAP) |
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Compound Nerve Action Potential |
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Repetitive Nerve Stimulation Test |
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Visual Evoked Potentials (VEP) |
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Brainstem Auditory Evoked Potentials |
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Somatosensory Evoked Potentials (SSEP) |
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Central Nervous System Degenerative Disorders |
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243 | (44) |
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Characteristics of Delirium (think delirium tremens) |
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Characteristics of Dementia |
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Relative Frequency of Types |
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Dementia and Delirium Quick Reference Table |
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General Management (Specifics depend on underlying cause) |
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Central Nervous System Degenerative Diseases |
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Inherited Ataxias---Early Onset |
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Inherited Ataxias---Late Onset |
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Degenerative Diseases of the Spinal Cord---Predominantly Upper Motor Neuron |
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Degenerative Diseases of the Spinal Cord---Predominantly Lower Motor Neuron |
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Degenerative Diseases of the Spinal Cord---Mixed Upper and Lower Motor Neuron |
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Definition, Phenomenology, and Classification |
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Specific Tremor Syndromes |
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Neurofibromatosis Type I (Peripheral) |
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Neurofibromatosis Type II (Central) |
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Sturge-Weber Syndrome (Encephalotrigeminal Angiomatosis) |
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Familial Telangiectasia (Osler-Rendu-Weber Syndrome) |
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Von Hippel-Lindau Disease (Hemangioblastoma of the Cerebellum) |
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Ataxia-Telangiectasia (Louis-Bar Syndrome) |
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Trinucleotide Repeat Diseases |
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Trinucleotide repeat diseases |
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Normal Age-Related Neurologic Changes |
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287 | (2) |
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Transplant Neurology---Complications |
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FK-506-similar to cyclosporin |
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Graft-Versus-Host Disease---usually in bone marrow transplant patients |
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289 | (6) |
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Tolosa-Hunt Syndrome (cavernous sinus syndrome) |
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Miller-Fisher Variant of Guillain-Barre Syndrome |
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Argyll-Robertson Syndrome |
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Intranuclear Ophthalmoplegia |
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295 | (34) |
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Headache Classification (Derived from the International Classification of Headache Disorders, 2nd Edition) |
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Tension-Type Headache (TTH) |
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Short-lasting Unilateral Neuralgiform Headache Attacks with Conjunctival Injection and Tearing (SUNCT) |
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New Daily Persistent Headache |
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Medication Overuse Headache |
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Primary Exertional Headache |
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Primary Headache Associated with Sexual Activity |
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Primary Thunderclap Headache (``crash'' migraine) |
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Glossopharyngeal Neuralgia |
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Headache of Aneurismal Subarachnoid Hemorrhage |
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Headache Associated with Vascular Dissection |
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Idiopathic Intracranial Hypertension (Pseudotumor Cerebrii) |
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Complex Regional Pain Syndromes |
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Laboratory/Imaging (not essential for diagnosis) |
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329 | (6) |
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Computed Tomograph Density |
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Computed Tomography in Stroke |
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Computed Tomography in Hemorrhage |
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High Precontrast Computed Tomography Density with Intense Contrast Enhancement |
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Magnetic Resonance Imaging |
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Enhancing Ventricular Margins |
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MRI Visualization of Myelination |
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Features of Hippocampal Sclerosis |
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Positron Emission Tomography |
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Single Proton Emission Computed Tomography (SPECT) |
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335 | (2) |
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Paraneoplastic Autoantibodies |
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Peripheral Neuropathy Antibodies |
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Autonomic Nervous System Testing |
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337 | (2) |
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Heart Rate Response to Deep Breathing (Cardiovagal-Parasympathetic) |
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Heart Rate Response to Standing |
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Tilt Table Testing (Adrenergic) |
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Blood Pressure Response to Hand Grip |
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Thermoregulatory Sweat Test |
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Quantitative Sudomotor Axon Reflex Test (QSART) |
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339 | (2) |
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Respiratory Patterns Associated with Coma |
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Pupillary Findings Associated with Coma |
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Elevated Intracranial Pressure Management |
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341 | (8) |
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Circadian Control of Sleep-Wakefulness |
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Sleep-Disordered Breathing |
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349 | (2) |
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Central and Peripheral Causes of Nystagmus |
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Characteristics of Central and Peripheral Nystagmus |
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Characteristics of Peripheral Causes of Vertigo |
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351 | (8) |
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Neuropsychologic Evaluation |
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359 | (4) |
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Generalized Convulsive Status Epilepticus---Treatment Protocol |
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Optional Confirmatory Tests |
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Medical Record Documentation |
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Brain Death Criteria in Children |
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Observation and Confirmatory Tests by Age |
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What Is Your Diagnosis? |
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Index |
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363 | |